POLYMYOSITIS DERMATOMYOSITIS
\pˌɒlɪmɪəsˈa͡ɪtɪs dˌɜːmɐtˌɒmɪəsˈa͡ɪtɪs], \pˌɒlɪmɪəsˈaɪtɪs dˌɜːmɐtˌɒmɪəsˈaɪtɪs], \p_ˌɒ_l_ɪ_m_ɪ__ə_s_ˈaɪ_t_ɪ_s d_ˌɜː_m_ɐ_t_ˌɒ_m_ɪ__ə_s_ˈaɪ_t_ɪ_s]\
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A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
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Nearby Words
- polymyodous
- polymyoid
- polymyositides
- polymyositis
- polymyositis dermatomyositides
- Polymyositis Dermatomyositis
- polymyositis ossificans
- polymyxin
- polymyxin b
- polymyxin b sulfate
- polymyxin e