MUCOPOLYSACCHARIDOSIS VI
\mjuːkˈɒpəlˌɪsɐkˌɑːɹɪdˈə͡ʊsɪs vˌiːˈa͡ɪ], \mjuːkˈɒpəlˌɪsɐkˌɑːɹɪdˈəʊsɪs vˌiːˈaɪ], \m_j_uː_k_ˈɒ_p_ə_l_ˌɪ_s_ɐ_k_ˌɑː_ɹ_ɪ_d_ˈəʊ_s_ɪ_s v_ˌiː__ˈaɪ]\
Word of the day
Procollagen Proline Dioxygenase
- mixed-function oxygenase that catalyzes hydroxylation prolyl-glycyl-containing-peptide, usually in protocollagen, hydroxyprolylglycyl-peptide. The enzyme utilizes molecular oxygen with a concomitant oxidative decarboxylation of 2-oxoglutarate to succinate. EC 1.14.11.2.