MARIE-ROBINSON SYNDROME

\mɐɹˈiːɹˈɒbɪnsən sˈɪndɹə͡ʊm], \mɐɹˈiːɹˈɒbɪnsən sˈɪndɹə‍ʊm], \m_ɐ_ɹ_ˈiː_ɹ_ˈɒ_b_ɪ_n_s_ə_n s_ˈɪ_n_d_ɹ_əʊ_m]\

Definitions of MARIE-ROBINSON SYNDROME

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Procollagen Proline Dioxygenase

  • mixed-function oxygenase that catalyzes hydroxylation prolyl-glycyl-containing-peptide, usually in protocollagen, hydroxyprolylglycyl-peptide. The enzyme utilizes molecular oxygen with a concomitant oxidative decarboxylation of 2-oxoglutarate to succinate. EC 1.14.11.2.
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