LANDOUZY'S DISEASE
\lˈanduːziz dɪzˈiːz], \lˈanduːziz dɪzˈiːz], \l_ˈa_n_d_uː_z_i_z d_ɪ_z_ˈiː_z]\
Definitions of LANDOUZY'S DISEASE
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Procollagen Proline Dioxygenase
- mixed-function oxygenase that catalyzes hydroxylation prolyl-glycyl-containing-peptide, usually in protocollagen, hydroxyprolylglycyl-peptide. The enzyme utilizes molecular oxygen with a concomitant oxidative decarboxylation of 2-oxoglutarate to succinate. EC 1.14.11.2.