HEINE-MEDIN DISEASE
\hˈe͡ɪnmˈɛdɪn dɪzˈiːz], \hˈeɪnmˈɛdɪn dɪzˈiːz], \h_ˈeɪ_n_m_ˈɛ_d_ɪ_n d_ɪ_z_ˈiː_z]\
Definitions of HEINE-MEDIN DISEASE
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Procollagen Proline Dioxygenase
- mixed-function oxygenase that catalyzes hydroxylation prolyl-glycyl-containing-peptide, usually in protocollagen, hydroxyprolylglycyl-peptide. The enzyme utilizes molecular oxygen with a concomitant oxidative decarboxylation of 2-oxoglutarate to succinate. EC 1.14.11.2.