PHENYLALANINE 4 MONOOXYGENASE
\fˌiːna͡ɪlˈalɐnˌa͡ɪn fˈɔː mˈɒnə͡ʊˌɒksɪd͡ʒənˌe͡ɪs], \fˌiːnaɪlˈalɐnˌaɪn fˈɔː mˈɒnəʊˌɒksɪdʒənˌeɪs], \f_ˌiː_n_aɪ_l_ˈa_l_ɐ_n_ˌaɪ_n f_ˈɔː m_ˈɒ_n_əʊ_ˌɒ_k_s_ɪ_dʒ_ə_n_ˌeɪ_s]\
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An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE, dihydrobiopterin, and water from L-PHENYLALANINE, tetrahydrobiopterin, and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL. EC 1.14.16.1.
By DataStellar Co., Ltd
Word of the day
tinctura quininae ammoniata
- A preparation made by dissolving quinin sulphate in alcohol [Br. Ph.].
Nearby Words
- phenylacetamide
- phenylacetic acid
- phenylalanin
- phenylalanine
- phenylalanine 4 hydroxylase
- Phenylalanine 4 Monooxygenase
- phenylalanine ammonia lyase
- phenylalanine hydroxylase
- phenylalanine hydroxylase deficiency disease
- phenylalanine hydroxylase deficiency disease, maternal
- phenylalanine hydroxylase deficiency disease, severe