Definitions of N Acetylgalactosamine 4 sulphate Sulphatase

  1.   An arylsulfatase that catalyzes the hydrolysis of the 4 sulfate groups of the N acetyl D galactosamine 4 sulfate units of chondroitin sulfate and dermatan sulfate A deficiency of this enzyme is responsible for the inherited lysosomal disease Maroteaux Lamy syndrome MUCOPOLYSACCHARIDOSIS VI EC 3 1 6 12