Definitions of N Acetylgalactosamine 4 Sulfatase
An arylsulfatase that catalyzes the hydrolysis of the 4- sulfate groups of the N- acetyl- D- galactosamine 4- sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux- Lamy syndrome ( MUCOPOLYSACCHARIDOSIS VI). EC 3. 1. 6. 12.