HYPERPLASTIC CHONDRODYSTROPHY
\hˌa͡ɪpəplˈastɪk kˈɒndɹədˌɪstɹəfi], \hˌaɪpəplˈastɪk kˈɒndɹədˌɪstɹəfi], \h_ˌaɪ_p_ə_p_l_ˈa_s_t_ɪ_k k_ˈɒ_n_d_ɹ_ə_d_ˌɪ_s_t_ɹ_ə_f_i]\
Definitions of HYPERPLASTIC CHONDRODYSTROPHY
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Procollagen Proline Dioxygenase
- mixed-function oxygenase that catalyzes hydroxylation prolyl-glycyl-containing-peptide, usually in protocollagen, hydroxyprolylglycyl-peptide. The enzyme utilizes molecular oxygen with a concomitant oxidative decarboxylation of 2-oxoglutarate to succinate. EC 1.14.11.2.