HUNTER SYNDROME GARGOYLISMS
\hˈʌntə sˈɪndɹə͡ʊm ɡˈɑːɡɔ͡ɪlˌɪzəmz], \hˈʌntə sˈɪndɹəʊm ɡˈɑːɡɔɪlˌɪzəmz], \h_ˈʌ_n_t_ə s_ˈɪ_n_d_ɹ_əʊ_m ɡ_ˈɑː_ɡ_ɔɪ_l_ˌɪ_z_ə_m_z]\
Definitions of HUNTER SYNDROME GARGOYLISMS
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Systemic lysosomal storage disease marked by progressive physical deterioration and caused by a deficiency of L-sulfoiduronate sulfatase. This disease differs from MUCOPOLYSACCHARIDOSIS I by slower progression, lack of corneal clouding, and X-linked rather than autosomal recessive inheritance. The mild form produces near-normal intelligence and life span. The severe form usually causes death by age 15.
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Board of Admiralty
- organized by Continental Congress, October 28, 1779, from earlier more numerous Committee. consisted two members Congress five others and had charge of all naval marine affairs. It was abolished February 7, 1781, upon the creation Secretary Marine.