GLYCOGEN DEBRANCHING ENZYME SYSTEM
\ɡlˈa͡ɪkəd͡ʒən dˈɛbɹant͡ʃɪŋ ˈɛnza͡ɪm sˈɪstəm], \ɡlˈaɪkədʒən dˈɛbɹantʃɪŋ ˈɛnzaɪm sˈɪstəm], \ɡ_l_ˈaɪ_k_ə_dʒ_ə_n d_ˈɛ_b_ɹ_a_n_tʃ_ɪ_ŋ ˈɛ_n_z_aɪ_m s_ˈɪ_s_t_ə_m]\
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1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.
By DataStellar Co., Ltd
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Nearby Words
- glycogen
- glycogen (starch) synthase
- glycogen branching enzyme
- glycogen debranching enzyme
- glycogen debranching enzyme deficiency
- Glycogen Debranching Enzyme System
- glycogen dextrin
- glycogen phosphorylase
- glycogen phosphorylase a, brain form
- glycogen phosphorylase a, liver form
- glycogen phosphorylase a, muscle form