DUCHENNE-ARAN'S DISEASE TYPE
\dˈʌt͡ʃənˈaɹənz dɪzˈiːz tˈa͡ɪp], \dˈʌtʃənˈaɹənz dɪzˈiːz tˈaɪp], \d_ˈʌ_tʃ_ə_n_ˈa_ɹ_ə_n_z d_ɪ_z_ˈiː_z t_ˈaɪ_p]\
Definitions of DUCHENNE-ARAN'S DISEASE TYPE
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Procollagen Proline Dioxygenase
- mixed-function oxygenase that catalyzes hydroxylation prolyl-glycyl-containing-peptide, usually in protocollagen, hydroxyprolylglycyl-peptide. The enzyme utilizes molecular oxygen with a concomitant oxidative decarboxylation of 2-oxoglutarate to succinate. EC 1.14.11.2.