BARTH'S HERNIA
\bˈɑːθz hˈɜːniə], \bˈɑːθz hˈɜːniə], \b_ˈɑː_θ_z h_ˈɜː_n_i__ə]\
Definitions of BARTH'S HERNIA
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Procollagen Proline Dioxygenase
- mixed-function oxygenase that catalyzes hydroxylation prolyl-glycyl-containing-peptide, usually in protocollagen, hydroxyprolylglycyl-peptide. The enzyme utilizes molecular oxygen with a concomitant oxidative decarboxylation of 2-oxoglutarate to succinate. EC 1.14.11.2.