ALDRICH SYNDROME
\ˈɔːldɹɪt͡ʃ sˈɪndɹə͡ʊm], \ˈɔːldɹɪtʃ sˈɪndɹəʊm], \ˈɔː_l_d_ɹ_ɪ_tʃ s_ˈɪ_n_d_ɹ_əʊ_m]\
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A rare, X-linked immunodeficiency syndrome characterized by eczema, thrombocytopenic purpura, and recurrent pyogenic infection. It is seen exclusively in young boys. Typically, IMMUNOGLOBULIN M levels are low and IMMUNOGLOBULIN A and IMMUNOGLOBULIN E levels are elevated. Lymphoreticular malignancies are common.
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